Butterfly disease: symptoms and therapies

Bullous epidermolysis, or butterfly disease, is a rare and dangerous disease. This is the genetic form of dermatitis, which is characterized by congenital defects in the structure of the skin. Unfortunately, to date, there is no effective treatment for such a violation.

Butterfly disease: causes and symptoms . As already mentioned, such a disease is hereditary in nature and manifests, as a rule, immediately after the birth of the child. What is the cause of this disease? First, you need to consider the structure of the skin of a normal person.

In humans, the top layer of the skin, or epidermis, is designed to protect against the influence of the external environment. It is in normal condition connected to a deeper sphere - the dermis. In patients diagnosed with "butterfly disease", there are no connections between the epidermis and the dermis, or are not strong enough to keep all layers of the skin together. That is why the skin of such a child is prone to injury.

Congenital bullous epidermolysis manifests itself immediately after birth. On the skin there are wounds and sores, even from the slightest external influence. If the child has something to do with it, then immediately a trace appears on the skin. Of course, butterfly disease is accompanied by constant pain.

As the disease progresses, the mucous membranes of the eyes, mouth and larynx are also affected, which makes it difficult for a child to eat. At a later stage, there may be a loss of teeth, damage to the mucosa of the esophagus and intestines.

Undoubtedly, the butterfly's disease itself is not deadly. But it's hard to live in such a state. In addition, persistent wounds, poorly healing sores and vesicles are excellent gates for fungal, bacterial and viral infections. In the absence of necessary care, the development of sepsis and the appearance of foci of necrosis.

Epidermolysis bullous: methods of treatment . Unfortunately, to date, the disease is incurable. The main methods of treatment are aimed at preventing infection and development of sepsis.

In some cases, the child needs regular therapy with glucocorticoid hormones. Such treatment helps to prevent the appearance of rashes and blisters on the skin, mucous membranes of internal organs. Sometimes it is also treated with immunomodulators that help the body fight infections.

A sick child needs constant care, which includes regular disinfection of wounds and dressings. The ranks are treated with olive oil, solutions of vitamins, ointments containing antibiotics, infusions of medicinal herbs. Very useful for diseased skin is a therapeutic bath with decoction of oak bark, alternatives, chamomile or a weak solution of potassium permanganate.

Particular attention should be paid to food. In the first months of life, breastfeeding is mandatory. In the future, the food should be liquid, without salt, spices or some irritating products. After feeding the baby must rinse his mouth with warm, digested water - this will prevent the appearance of vesicles and suppuration on the gums.

Shoes and clothes should be as soft as possible and made exclusively of natural fabrics. If the bones are not deformed, the child must move - this will help to prevent the appearance of contractures.

Butterfly disease is often accompanied by the development of anemia, which is extremely dangerous for a sick child. That's why you need constant monitoring of the blood condition, and if necessary - transfusion of plasma and albumins.

Sometimes the treatment uses "Tocopherol acetate" - a drug that stimulates the production of elastic and collagen fibers of the dermis. The therapy is carried out in several stages and involves several repeated courses. For some patients, this treatment has become a salvation.

In any case, butterfly disease is a very serious disease that needs constant treatment.